Synonym(s): - OODD
Classification (Orphanet): - Rare developmental defect during embryogenesis - Rare genetic disease - Rare odontologic disease - Rare skin disease Entire classification		Classification (ICD10): - Congenital malformations, deformations and chromosomal abnormalities - See
Epidemiological data: Class of prevalence: <1 / 1 000 000 Average age onset: childhood Average age of death: normal Type of inheritance: autosomal recessive		External references: 1 OMIM reference - See 1 MeSH reference: C537742
More Info - Orphanet

Gene symbol	UniProt reference	OMIM reference
WNT10A	Q9GZT5	606268

- Abnormal hair texture / hair dysplasia
- Anodontia / oligodontia / hypodontia
- Autosomal recessive inheritance
- Cutaneous rash
- Decreased body hair / axillar / pubic hairlessness
- Dental malocclusion
- Dysplastic / thick / grooved fingernails
- Dysplastic / thick / grooved toenails
- Erythema / erythematous lesions / erythroderma / polymorphous erythema
- Hyperhidrosis / increased sweating
- Hypotrichosis / atrichia / atrichiasis / scalp hairlessness
- Palmoplantar hyperkeratosis / keratoderma
- Tooth shape anomaly
- Urticaria

- Absent / decreased / thin eyebrows
- Acanthosis nigricans
- Anomalies of tongue, gingiva and oral mucosa
- Blepharitis / eyelid inflammation
- Chronic uveitis / blepharitis / episcleritis / scleritis / conjonctivitis / keratitis
- Photophobia
- Skin photosensitivity
- Telangiectasiae of the skin

- Skin / cutaneous neoplasm / tumor / carcinoma / cancer (excluding melanoma)